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Description |
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A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
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Synonyms |
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CJD Variant (V-CJD)
New Variant Creutzfeldt-Jakob Disease
Spongiform Encephalopathy, Subacute
CJD
CJD (Creutzfeldt-Jakob Disease)
Creutzfeldt-Jakob Disease
Creutzfeldt-Jakob Disease, Familial
Creutzfeldt-Jakob Disease, New Variant
Familial Creutzfeldt-Jakob Disease
Jakob-Creutzfeldt Disease
Jakob-Creutzfeldt Syndrome
V-CJD (Variant-Creutzfeldt-Jakob Disease)
CJD (Creutzfeldt Jakob Disease)
CJD Variant (V CJD)
CJD Variants (V-CJD)
CJDs (Creutzfeldt-Jakob Disease)
Creutzfeldt Jakob Disease
Creutzfeldt Jakob Disease, Familial
Creutzfeldt Jakob Disease, New Variant
Creutzfeldt Jakob Syndrome
Creutzfeldt-Jakob Diseases, Familial
Disease, Creutzfeldt-Jakob
Disease, Familial Creutzfeldt-Jakob
Disease, Jakob-Creutzfeldt
Encephalopathies, Subacute Spongiform
Encephalopathy, Subacute Spongiform
Familial Creutzfeldt Jakob Disease
Familial Creutzfeldt-Jakob Diseases
Jakob Creutzfeldt Disease
Jakob Creutzfeldt Syndrome
New Variant Creutzfeldt Jakob Disease
Spongiform Encephalopathies, Subacute
Subacute Spongiform Encephalopathies
Subacute Spongiform Encephalopathy
Syndrome, Creutzfeldt-Jakob
Syndrome, Jakob-Creutzfeldt
Variant, CJD (V-CJD)
Variants, CJD (V-CJD)
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Tree Numbers |
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C10.228.140.380.165
C10.228.228.800.230
F03.087.400.300
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